Malignant atrophic papulosis is an uncommon vasculopathy that affects the skin, gastrointestinal tract, and nervous system. The systemic variant has a rapid clinical course and a high death rate. Occlusive small vessel vasculopathy is a kind of malignant atrophic papulosis. Blood arteries supplying the epidermis, gastrointestinal tract, and central nervous system are among those impacted. Degos disease is another name for malignant atrophic papulosis.
- Malignant atrophic papulosis is an extremely rare condition.
- However, it is found to be most common in young Caucasian individuals, but it has been documented in people of many ethnicities and ages.
- In the medical literature, around 200 cases of Degos illness have been described. The disorder's exact prevalence is unknown.
- Many experts believe that Degos illness is underdiagnosed, making determining its true prevalence in the general population challenging.
- Degos disease can afflict people of any age, but it is more frequent in teenagers and young adults.
- Males have been impacted more frequently than females in the recorded cases.
- However, one study discovered that women were more likely than males to have the benign cutaneous variant of Degos disease.
Skin lesions,Abdominal pain,Gastrointestinal bleeding,Strokes,Headaches,Memory loss or altered sensation
Perforation of the bowel,Epilepsy